A fibromuscular dysplasia clinical tetrad of coronary artery dissection, cardiogenic shock, carotid dissection, and stroke.
Author
Klinkhammer, Brent.
Publisher
Oman Medical Specialty Board.
English abstract
Spontaneous coronary artery dissection is a serious and underreported clinical entity
strongly associated with fibromuscular dysplasia (FMD). The female predominance of
FMD may predispose many women to coronary artery dissection or other similar vascular
pathologies. We present a case of a young woman who presented with a clinical tetrad
of spontaneous coronary artery dissection, cardiogenic shock requiring extracorporeal
membrane oxygenation, internal carotid dissections, and subacute cerebellar infarct
secondary to underlying FMD. The patient's clinical course and vascular pathology
are discussed. A review of the relevant literature of previously published similar cases,
the incidence of spontaneous coronary artery dissection, and issues in the clinical
management of spontaneous coronary artery dissection are also included.
