English abstract
Neurofibromatosis type 1 (NF1) (von Recklinghausen's disease) is an autosomal
dominant disorder characterized by café-au-lait spots, pigmented hamartomas of the iris,
and multiple neurofibromas. Patients can present with hemorrhage secondary to trauma
or rarely with spontaneous hemorrhage, both of which can be lethal and life-threatening.
We report a 14-year-old girl with a rapidly expanding hematoma in a rare presentation
of spontaneous bleed into the NF1 lesion in her scalp. Soon after presentation, she went
into hemorrhagic shock. Emergency coiling of the left maxillary artery and branches
successfully arrested the bleeding, while resuscitation reversed the hemorrhagic shock.
