Cornual ectopic pregnancy is a rare form of ectopic pregnancy but has catastrophic presentation when diagnosis is missed. It is usually misdiagnosed as degenerated myoma at uterine fundus but can be differentiated by positive pregnancy test, absence of intrauterine gestational sac and diagnostic laparoscopy when necessary. In this case, we present a case of cornual ectopic pregnancy diagnosed by serial serum beta subunit of human chorionic gonadotropin, vaginal ultrasound and diagnostic laparoscopy, which was managed by evacuation of the cornual ectopic by laparotomy, excision of the tube and then suturing the pedicle adjacent to the uterine wall.