Ocular sebaceous carcinoma is a rare condition and accounts for 1% to 5.5% of eyelid malignancies and is the third most common eyelid malignancy after basal cell and squamous cell carcinoma. It usually affects elderly women, has a high rate of local recurrence, and a tendency to regional and distant metastases. The authors hereby describe a 51-year- old female who was presented with the typical symptoms and signs of peri-ocular malignancy. Histopathologic evaluation from the excised involved area confirmed the diagnosis of ocular sebaceous carcinoma.