وثيقة

Prepubertal hypertransfusion in thalassemia intermedia : sustained positive effects on growth, splenic function and endocrine parameters.

المعرف
DOI 10. 5001/omj.2012.125
مؤلف
المساهمون
Daar, Shahina., مؤلف
Wali, Yasser., مؤلف
الناشر
Oman Medical Specialty Board.
ميلادي
2012-11
اللغة
الأنجليزية
الملخص الإنجليزي
We report a known case of thalassemia intermedia (Hb Dhofar) who in spite of mild thalassemic facies, attained his normal genetic height, pubertal maturity and improved self-image with minimal splenomegaly through a hypertransfusion/chelation regimen that was started just before puberty and maintained for 5 years. As there are no clear guidelines in the management of patients with thalassemia intermedia, the option of hypertransfusion/chelation during the pubertal growth spurt may alleviate some of the complications associated with thalassemia intermedia.
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Tony, Surekha, Daar, Shahina, Zachariah, Mathew, & Wali, Yasser (2012). Prepubertal hypertransfusion in thalassemia intermedia : sustained positive effects on growth, splenic function and endocrine parameters. Oman Medical Journal, 27 (6), [1-3].
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